Skip to main content

Table 5 Classification of Angioedema

From: WAO Guideline for the Management of Hereditary Angioedema

Bradykinin-Induced AE

Mast Cell Mediator-Induced AE

 

C1-INH Deficiency/Defect

C1-INH Normal

IgE Mediated

Non-IgE Mediated

Unknown Mediator Idiopathic AE

Inherited

Acquired

Inherited

Acquired

Angioedema with anaphylaxis Urticaria

Angioedema with urticaria

--

HAE-1

AAE

HAE-3

ACE-I

--

--

--

HAE-2

      
  1. AAE, acquired angioedema due to C1 inhibitor deficiency; ACE-I, angiotensin-converting enzyme-induced angioedema; AE, angioedema; HAE-1, hereditary angioedema due to C1 inhibitor deficiency; HAE-2, hereditary angioedema due to C1 Inhibitor defect; HAE-3, hereditary angioedema with normal C1 inhibitor levels.