From: WAO Guideline for the Management of Hereditary Angioedema
Bradykinin-Induced AE | Mast Cell Mediator-Induced AE | Â | ||||
---|---|---|---|---|---|---|
C1-INH Deficiency/Defect | C1-INH Normal | IgE Mediated | Non-IgE Mediated | Unknown Mediator Idiopathic AE | ||
Inherited | Acquired | Inherited | Acquired | Angioedema with anaphylaxis Urticaria | Angioedema with urticaria | -- |
HAE-1 | AAE | HAE-3 | ACE-I | -- | -- | -- |
HAE-2 | Â | Â | Â | Â | Â | Â |