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Table 2 Assays for C1 INH Deficiency

From: Angioedema

 

C1 INH Protein

C1 Function

C4

C1Q

95 kd C1 INH

Hereditary type 1

↓

↓

↓

N

No

Hereditary type 2

N or ↑

↓

↓

N

No

Acquired type 1

↓

↓

↓

↓

No

Acquired type 2

↓

↓

↓

↓

Yes